What is splenic lymphangioma?
Splenic lymphangioma is a rare malformation of the splenic lymphatic channels, mostly seen in children. It is characterized by the presence of cysts, resulting from increases in the size and number of thin-walled lymphatic vessels that are abnormally interconnected and dilated.
What is lymphangioma cyst?
Lymphangiomas, also called lymphatic malformations, are noncancerous, fluid-filled cysts that occur in lymphatic vessels. These vessels contain a substance called lymph, and together they make up the lymphatic system.
What is splenic cyst?
Splenic epithelial cysts, also known as splenic epidermoid cysts or primary splenic cysts, are unilocular fluid lesions with thin and smooth walls and no enhancement. They represent ~20% of cysts found in the spleen, and are usually an innocuous incidental imaging finding.
What causes lymphangioma cystic?
Congenital lymphangiomas form due to blockage of the lymphatic system during fetal development, though the cause remains unknown. Cystic lymphangiomas are associated with genetic disorders, including trisomies 13, 18, and 21, Noonan syndrome, Turner syndrome, and Down syndrome.
How is Lymphangioma treated?
The preferred treatment for lymphangiomas is complete surgical excision. On the basis of the Whimster hypothesis, the large subcutaneous cisterns should be removed to prevent the lesion from resurfacing. Local recurrences are common in lymphangiomas.
What is spleen hemangioma?
Splenic hemangiomas are rare lesions, but they are the most common benign primary tumor of the spleen. b. Splenic hemangiomas are the only type of vascular tumor that occurs in the spleen. c. Splenic hemangiomas are almost always symptomatic and are rarely identified incidentally.
How is cystic lymphangioma diagnosed?
Retroperitoneal cystic lymphangiomas are rare tumors of the lymphatic system. These tumors usually present in childhood and are often diagnosed incidentally with imaging procedures.
What causes cyst spleen?
The vast majority of splenic cysts in the United States are pseudocysts resulting from blunt trauma. Other causes include infarction or infection. Often the inciting event cannot be recalled.
How serious is a cyst on spleen?
Symptomatic splenic cysts have been considered as high-risk lesions for future automatic rupture, which explains why most authors include them in the indications for surgical treatment (either splenectomy or more conservative operations) [7]-[9].
What is the treatment for lymphangioma?
Is lymphangioma malignant?
Acquired lymphangiomas may result from trauma, inflammation, or lymphatic obstruction. Most lymphangiomas are benign lesions that result only in a soft, slow-growing, “doughy” mass. Since they have no chance of becoming malignant, lymphangiomas are usually treated for cosmetic reasons only.
What are the characteristics of cystic lymphangioma of the spleen?
This report concerns a case of cystic lymphangioma of the spleen, consisting of a large splenic cyst with associated multiple, small, subcapsular cysts and lymphangiectasia. The cysts are lined by endothelium, and they conform to the characteristics of dilated lymphatic channels.
Should splenic lymphangiomas be included in the differential diagnosis of splenic cysts?
This case indicates that splenic lymphangiomas should be considered in the differential diagnosis of splenic cystic masses, even in adults, and should be managed with splenectomy once diagnosed to prevent complications.
What is a lymphangioma?
Lymphangiomas are uncommon, benign malformations of the lymphatic system that can occur anywhere on the skin and mucous membranes. Lymphangiomas can be categorized as deep or superficial based on the depth and size of the abnormal lymphatic vessels or as congenital or acquired.
How common are splenic cysts of the spleen?
Splenic cysts are uncommon, with fewer than 600 cases reported in the world literature. This report concerns a case of cystic lymphangioma of the spleen, consisting of a large splenic cyst with associated multiple, small, subcapsular cysts and lymphangiectasia.